Ichthyosis Uterus – A Rare Premalignant Lesion of Endometrium

Ichthyosis (ikTHeosis) uterus is a rare benign metaplastic transformation of uterine endometrium into stratified squamous epithelium. The word ichthyosis (plural ichthyoses) comes from two ancient Greek (ixtus), meaning fish and disease. epithelium parakeratotic with absent granular layer. Premalignant potential this has not been established due to the rarity occurrence. We report case 72 year old female, post menopausal complaints painless lower abdominal distension for past six months. She had no history menorrhagia or dysmenorrhea in her previous menstrual cycles. USG abdomen was done. taken up elective hysterectomy diagnosis hydrometra. Total bilateral salpingo-oophorectomy pelvic lymph node sampling Peritoneal fluid cytology, peritoneal biopsy Gross section specimen seen same sent histopathological examination. Based on these histological findings uteri focal High grade Squamous intraepithelial lesion made. In our case, there direct continuity metaplasia endocervix endometrial lining. This supports spread zone cervix cavity. However, stimulation as result long term hydrometra being hypothesised patient. association hydrometra, dysplastic changes are speculated.